Hypergonadotropic hypogonadism and cerebellar ataxia: an unusual association
نویسندگان
چکیده
منابع مشابه
Hypergonadotropic hypogonadism and cerebellar ataxia: an unusual association.
Federal University of São Paulo (UNIFESP), São Paulo SP, Brazil: Department of Neurology and Neurosurgery; Department of Endocrinology; Department of Ophthalmology. The association between cerebellar ataxia and hypogonadism was first described by Gordon Holmes in 1907. It represents a highly heterogenous syndrome with insidious onset. The hypogonadism of most patients with Gordon Holmes syndrom...
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The association of ataxia, hypergonadotropic hypogonadism and hearing loss is extremely rare. Considerable heterogeneity exists in the literature of the neurological manifestations, age of onset, clinical severity and associated abnormalities. We describe a 24-year-old woman with secondary hypergonadotropic amenorrhea, early-onset progressive spinocerebellar ataxia (SCA), late-onset sensorineur...
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ژورنال
عنوان ژورنال: Arquivos de Neuro-Psiquiatria
سال: 2010
ISSN: 0004-282X
DOI: 10.1590/s0004-282x2010000100028